Ravjit Singh
Prince Of Wales Hospital, Australia
Title: Implantation & Outcomes in X Linked Stapes Gusher Syndrome
Biography
Biography: Ravjit Singh
Abstract
X-Linked Gusher Syndrome occurs at the point of vestibule opening, with an associated rush of perilymph first reported by Sennaroglu et al 2006. Initially, the presence of the characteristic radiological features was a contraindication to cochlea implantation but recent reports have demonstrated successful implantation. The postoperative outcomes of these implantations have been variable, with expressive language and speech intelligibility ratings being improved from pre-operatively but poor compared to normal cohort. We present our experiences of four ears who underwent Cochlea implantation with intra-operative gusher syndrome.